Pigmented purpuric dermatosis refers to one of the three major classes of skin conditions characterized by
purpuric skin eruptions.
Pigmented purpuric dermatosis are distinguished from other
purpura
Purpura () is a condition of red or purple discolored spots on the skin that do not blanch on applying pressure. The spots are caused by bleeding underneath the skin secondary to platelet disorders, vascular disorders, coagulation disorders, ...
by size (0.3–1 cm) and are most often seen in the lower extremities.
Pigmentary purpuric eruptions may present with one of several clinical patterns. There may be overlapping characteristics among pigmented purpuric dermatosis and between their signs and those of other
purpuric eruptions.
Examples of the pigmented purpuric dermatosis group include:
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Schamberg's disease
Schamberg's disease, (also known as "progressive pigmentary dermatosis of Schamberg", "purpura pigmentosa progressiva" (PPP), and "Schamberg's purpura") is a chronic discoloration of the skin found in people of all ages, usually only affecting ...
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Majocchi's disease
Majocchi's disease, also known as Purpura annularis telangiectodes of Majocchi is a not-well-recognized and uncommon skin condition characterized by purple/bluish-red 1- to 3-cm annular patches composed of dark red telangiectases with petechiae. ...
(Purpura annularis telangiectodes)
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Gougerot-Blum syndrome (Pigmented purpuric lichenoid dermatitis)
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Ducas and Kapetanakis pigmented purpura
Doucas and Kapetanakis pigmented purpura is a skin condition characterized by scaly and eczematous patches, which also have petechiae and hemosiderin
Hemosiderin image of a kidney viewed under a microscope. The brown areas represent hemosiderin ...
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Lichen aureus
Lichen aureus is a skin condition characterized by the sudden appearance of one or several golden or rust-colored, closely packed macule
A skin condition, also known as cutaneous condition, is any medical condition that affects the integumenta ...
Although vascular damage may be present, it is insufficient for these conditions to be considered forms of
vasculitis
Vasculitis is a group of disorders that destroy blood vessels by inflammation. Both arteries and veins are affected. Lymphangitis (inflammation of lymphatic vessels) is sometimes considered a type of vasculitis. Vasculitis is primarily caused b ...
.
A few very small non-blinded studies of treatment with narrow-band ultraviolet light have been reported as promising.
[Summarized in 2015 by Tapan Kumar Dhali, Monica Chahar, and Mohammad Asad Haroon in]
Phototherapy as an effective treatment for Majocchi's disease - Case report
An Bras Dermatol. 2015 Jan-Feb; 90(1): 96–99.
See also
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Purpura
Purpura () is a condition of red or purple discolored spots on the skin that do not blanch on applying pressure. The spots are caused by bleeding underneath the skin secondary to platelet disorders, vascular disorders, coagulation disorders, ...
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Skin lesion
A skin condition, also known as cutaneous condition, is any medical condition that affects the integumentary system—the organ system that encloses the body and includes skin, nails, and related muscle and glands. The major function of this s ...
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List of cutaneous conditions
Many skin conditions affect the human integumentary system—the organ system covering the entire surface of the body and composed of skin, hair, nails, and related muscle and glands. The major function of this system is as a barrier against t ...
References
External links
Vascular-related cutaneous conditions
{{Cutaneous-condition-stub