Persistent tunica vasculosa lentis is a

congenital A birth defect, also known as a congenital disorder, is an abnormal condition that is present at birth regardless of its cause. Birth defects may result in disabilities that may be physical, intellectual, or developmental. The disabilities can ...

ocular Eyes are organs of the visual system. They provide living organisms with vision, the ability to receive and process visual detail, as well as enabling several photo response functions that are independent of vision. Eyes detect light and con ...

anomaly. It is a form of persistent hyperplastic primary vitreous (PHPV). It is a developmental disorder of the

vitreous Vitreous may refer to: Materials * Glass, an amorphous solid material ** Vitreous enamel, a material made by fusing powdered glass to a substrate by firing * Vitreous lustre, a glassy luster or sheen on a mineral surface Biology * Vitreous body, ...

. It is usually unilateral and first noticed in the

neonatal An infant or baby is the very young offspring of human beings. ''Infant'' (from the Latin word ''infans'', meaning 'unable to speak' or 'speechless') is a formal or specialised synonym for the common term ''baby''. The terms may also be used to ...

period. It may be associated with

microphthalmos Microphthalmia (Greek: grc, μικρός, mikros, small, label=none, grc, ὀφθαλμός, ophthalmos, eye, label=none, also referred as microphthalmos, is a developmental disorder of the eye in which one (unilateral microphthalmia) or both ( ...

cataracts A cataract is a cloudy area in the lens of the eye that leads to a decrease in vision. Cataracts often develop slowly and can affect one or both eyes. Symptoms may include faded colors, blurry or double vision, halos around light, trouble w ...

, and increased intraocular pressure. Elongated

ciliary processes The ciliary processes are formed by the inward folding of the various layers of the choroid, viz. the choroid proper and the lamina basalis, and are received between corresponding foldings of the suspensory ligament of the lens. Anatomy The ...

are visible through the dilated pupil. A USG B-scan confirms diagnosis in the presence of a cataract.

References

* http://www.djo.harvard.edu/files/1568.pdf * Wright KW, Speigel PH, Buckley EG. Pediatric Ophthalmology and Strabismus. Springer; US, New York: 2003. p. 17. Eye diseases {{eye-disease-stub

See also

References