Pagetoid reticulosis (also known as "acral mycoses fungoides",
"localized epidermotropic reticulosis",
"mycosis fungoides palmaris et plantaris",
"unilesional mycosis fungoides",
and "Woringer–Kolopp disease"
) is a cutaneous condition, an uncommon lymphoproliferative disorder, sometimes considered a form of
mycosis fungoides
Mycosis fungoides, also known as Alibert-Bazin syndrome or granuloma fungoides, is the most common form of cutaneous T-cell lymphoma. It generally affects the skin, but may progress internally over time. Symptoms include rash, tumors, skin lesion ...
.
Symptoms and Signs
Lesions emerge as well-demarcated psoriasiform or hyperkeratotic patches and plaques, with a central clearing and an elevated border. Pagetoid reticulosis is a very slow progressive variant of mycosis fungoides and is usually localized unlike the latter.
Treatment
The most common method of treatment includes
radiotherapy
Radiation therapy or radiotherapy, often abbreviated RT, RTx, or XRT, is a therapy using ionizing radiation, generally provided as part of cancer treatment to control or kill malignant cells and normally delivered by a linear accelerator. Radia ...
and/or surgical excision.
See also
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Pagetoid
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Cutaneous T-cell lymphoma
*
List of cutaneous conditions
Many skin conditions affect the human integumentary system—the organ system covering the entire surface of the body and composed of skin, hair, nails, and related muscle and glands. The major function of this system is as a barrier against t ...
References
External links
Lymphoid-related cutaneous conditions
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